Sacrococcygeal teratoma (SCT) is a congenital neoplasm that develop embryologically from totipotent cells and enlarge as a mass in sacrococcygeal region. SCT is usually benign but in a significant number of patients it presents with metastatic disease. A 1-year-old female child presented to our hospital with a history of a sacrococcygeal swelling since birth. Investigations revealed the lump to be a sacrococcygeal teratoma. The size of swelling increased gradually over time to a size of 12 cm × 9 cm at presentation. On further work up the patient was found to have metastasis in cerebrospinal fluid (CSF). We present a very rare case of CNS metastasis in a girl with sacrococcygeal teratoma reported on cytology.